Choice of surgical treatment for rhegmatogenous retinal detachment complicated with Wagner syndrome *
Features of Wagner syndrome include vitreous pathology characterized by an empty vitreous cavity, membranous vitreous opacity and strands, progressive chorioretinal atrophy and mild myopia. This syndrome has no systemic disorders, whereas other vitreoretinal degenerations have oculo-systemic disorders. Wagner syndrome generally has autosomal dominant inheritance. The complication of this syndrome that most frequently occurs is rhegmatogenous retinal detachment in childhood, which often has a poor prognosis after surgery. A 19-year-old man with myodesopsia in both eyes developed rhegmatogenous retinal detachment with oral dialysis of his left eye three months after his first visit. He had no family history of this syndrome. However, based on clinical findings, we made a diagnosis of Wagner syndrome and performed vitrectomy with scleral buckling on the patient’s rhegmatogenous retinal detachment with strong vitreal traction. No recurrence of rhegmatogenous retinal detachment was observed after complete reattachment during surgery. We usually employ scleral buckling or encircling for young people whose rhegmatogenous retinal detachment has no posterior vitreous detachment or macular detachment, for the purpose of creating a vitreal tamponade. However, we could effectively reduce the vitreal traction by employing vitrectomy with encircling to prevent the recurrence of retinal detachment for this case with mostly empty vitreous cavity and strong vitreal traction at the vitreous base. (Accepted on June 27, 2014)
